Systemic capillary leak syndrome (SCLS)

RecommendationsIG may be used for prevention of recurrent, life-threatening episodes, in addition to other therapies.
Dose/Frequency of Administration1 to 2 g/kg adjusted body weight divided over 2 to 5 days (maximum 1 g/kg/day), every 4 weeks.
 
Once the patient’s condition has stabilized, consider titrating the dose and/or the treatment interval to the lowest dose necessary to maintain clinical effectiveness.