Juvenile Idiopathic Inflammatory Myopathy (J-IIM)(Previously Juvenile Dermatomyositis)

RecommendationsIVIG is recommended when there is a lack of response or contraindication to corticosteroids, Methotrexate and/or Azathioprine therapy.
 
1st line: Corticosteroids and Methotrexate
2nd line: IVIG
3rd line: Cyclosporine
Dose/Frequency of AdministrationInitial: Total dose of 2 g/kg divided over 2 days.
 
Maintenance dose: A systematic approach should be taken to determine minimum effective dose.
 
Maximum dose should not exceed 2 g/kg